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New review highlights principles of nutrition management of inherited metabolic disorders

Date:
June 16, 2015
Source:
American Society for Parenteral and Enteral Nutrition (A.S.P.E.N.)
Summary:
The basic principles of chronic nutrition management of inherited metabolic disorders have been highlighted in a new article.
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Thanks to screening of newborns and newly developed therapies, the population of patients with inherited metabolic disorders has expanded. As these patients age and enter adulthood, diet therapy will be the mainstay of treatment for their disorders.

A new review, published in Nutrition in Clinical Practice (NCP), a peer-reviewed, interdisciplinary journal of the American Society for Parenteral and Enteral Nutrition (A.S.P.E.N.) that publishes articles about the scientific basis and clinical application of nutrition and nutrition support, highlights the basic principles of chronic nutrition management of inherited metabolic disorders.

"Failure to follow specific dietary treatment can lead to complications and even death in individuals with metabolic disorders," said Jeanette Hasse, PhD, RD, FADA, CNSC, Editor-in-Chief, NCP. "This review not only summarizes key concepts about several inborn errors of protein, carbohydrate, and fat metabolism, but also outlines the main principles of dietary treatment. This is a 'must-read' article for any nutrition professional who may provide care to individuals with a metabolic disorder."

Dietary therapy is critical for normal growth and development, to prevent acute complications, and/or to prevent long-term complications of the given disorder. Therapy is customized for the specific disorder and individualized for each patient to promote compliance.

Because nutrition therapy for patients with inherited metabolic disorders is lifelong, registered dietitians trained in the area of rare metabolic disorders are an essential part of the multi-disciplinary team including nurses, physicians, social workers, and other healthcare providers that delivers care for these patients.


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Materials provided by American Society for Parenteral and Enteral Nutrition (A.S.P.E.N.). Note: Content may be edited for style and length.


Journal Reference:

  1. S. W. Boyer, L. J. Barclay, L. C. Burrage. Inherited Metabolic Disorders: Aspects of Chronic Nutrition Management. Nutrition in Clinical Practice, 2015; DOI: 10.1177/0884533615586201

Cite This Page:

American Society for Parenteral and Enteral Nutrition (A.S.P.E.N.). "New review highlights principles of nutrition management of inherited metabolic disorders." ScienceDaily. ScienceDaily, 16 June 2015. <www.sciencedaily.com/releases/2015/06/150616072321.htm>.
American Society for Parenteral and Enteral Nutrition (A.S.P.E.N.). (2015, June 16). New review highlights principles of nutrition management of inherited metabolic disorders. ScienceDaily. Retrieved May 23, 2017 from www.sciencedaily.com/releases/2015/06/150616072321.htm
American Society for Parenteral and Enteral Nutrition (A.S.P.E.N.). "New review highlights principles of nutrition management of inherited metabolic disorders." ScienceDaily. www.sciencedaily.com/releases/2015/06/150616072321.htm (accessed May 23, 2017).

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